||Although the auricle forms earlier than the definitive external ear canal in the embryo, there may, on occasion, be cartilaginous malformation of both areas. Partial absence of the external ear and atresia of the external auditory canal are frequently associated with malformations of the middle ear, whereas the inner ear is usually normal.
This unilateral malformation of the auricular cartilage has produced a broad, overhanging helix that partially covers the antihelix. The antihelix is in high relief and superiorly displaced, resulting in a narrow scapha and a widened cymba conchae auriculae. The cavum conchae is narrow and the external auditory canal partially narrowed. There was an associated 60 decibel congenital conductive hearing loss in this ear.